Full metadata record
DC Field | Value | Language |
---|---|---|
dc.creator | Álvarez-Cienfuegos, J. (Javier) | - |
dc.creator | Baixauli-Fons, J. (Jorge) | - |
dc.creator | Zozaya-Larequi, G. (Gabriel) | - |
dc.creator | Bueno, A. (Álvaro) | - |
dc.creator | Blasco-Blanco, M. (Manuel) | - |
dc.creator | Martinez-Regueira, F. (Fernando) | - |
dc.creator | Angós, R. (Ramón) | - |
dc.creator | Hernandez-Lizoain, J.L. (Jose Luis) | - |
dc.creator | Idoate, M.A. (Miguel Ángel) | - |
dc.date.accessioned | 2012-03-26T14:48:10Z | - |
dc.date.available | 2012-03-26T14:48:10Z | - |
dc.date.issued | 2009 | - |
dc.identifier.citation | Cienfuegos JA, Baixauli J, Zozaya G, Bueno A, Arredondo J, Regueira FM, et al. Peutz-Jeghers syndrome and duodeno-jejunal adenocarcinoma--therapeutic implications. Rev Esp Enferm Dig 2009 Dec;101(12):875-879. | es_ES |
dc.identifier.issn | 1130-0108 | - |
dc.identifier.uri | https://hdl.handle.net/10171/21346 | - |
dc.description.abstract | The Peutz-Jeghers syndrome (PJS) is an autosomal dominant hamartomatous poliposis describred in 1921. Hemminki in 1997 described the presence of LKB-1 mutation tumor-suppressor gen.The patients with PJS develop a higher cumulative incidence of gastrointestinal, pancreas and extraintestinal tumors, being occasion of a renew interest on hamartomatous polyposis syndromes regarding the clinical care, cancer surveillance treatment and long term follow-up.We report the case of a 38 years old male, diagnosed of PJS who developed a multiple adenocarcinoma in duodenum and yeyunum. Surgically treated and with a long-term free disease survival of 11 years represents the sixth case reported in the spanish literature of PJS associated with a gastrointestinal tumor.A critical review, molecular alterations and the established criteria of tumor screening and surveillance are reviewed. | es_ES |
dc.language.iso | spa | es_ES |
dc.publisher | Arán Ediciones | es_ES |
dc.rights | info:eu-repo/semantics/openAccess | es_ES |
dc.subject | Peutz-Jeghers syndrome | es_ES |
dc.subject | Hamartomatous | es_ES |
dc.subject | Carcinogenesis | es_ES |
dc.subject | Intestinal polyposis | es_ES |
dc.subject | Hereditary cancer | es_ES |
dc.title | Peutz-Jeghers syndrome and duodeno-jejunal adenocarcinoma-therapeutic implications | es_ES |
dc.type | info:eu-repo/semantics/article | es_ES |
dc.relation.publisherversion | http://www.reed.es/numero_actual.php?volumen=101&numero=12 | es_ES |
dc.type.driver | info:eu-repo/semantics/article | es_ES |
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